A Case of Primary Angiitis of the Central Nervous System: A Case Presentation
Journal of the Korean Society of Emergency Medicine
;
: 329-332, 2003.
Artigo
em Coreano
| WPRIM
| ID: wpr-82054
ABSTRACT
Primary angiitis of the central nervous system (PACNS) is a rare idiopathic disorder with recurrent vasculitis restricted to the central nervous system (CNS) and involves small-sized (and at time medium-sized) blood vessels. The typical clinical manifestations include multifocal strokes or encephalopathy, often associated with severe headaches. There are very few pediatric cases with PACNS reported in the literature. The diagnosis of PACNS is mainly based on its clinical features, demonstration of angiitis on angiography or biopsy, and exclusion of secondary causes of angiitis. A high index of suspicion is necessary for the diagnosis. Though the prognosis is generally poor, use of steroids and immunosuppressive therapy has been useful in achieving successful remission in many patients. We report the case of a patient with PACNS presenting recurrent headaches for 5 days.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Prognóstico
/
Esteroides
/
Vasculite
/
Biópsia
/
Vasos Sanguíneos
/
Angiografia
/
Sistema Nervoso Central
/
Acidente Vascular Cerebral
/
Diagnóstico
/
Cefaleia
Tipo de estudo:
Estudo diagnóstico
/
Estudo prognóstico
Limite:
Humanos
Idioma:
Coreano
Revista:
Journal of the Korean Society of Emergency Medicine
Ano de publicação:
2003
Tipo de documento:
Artigo
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