Lupus Anticoagulant-hypoprothrombinemia Syndrome as an Initial Manifestation of Systemic Lupus Erythematosus: A Case Report / 임상소아혈액종양
Clinical Pediatric Hematology-Oncology
; : 145-148, 2014.
Article
em Ko
| WPRIM
| ID: wpr-84411
Biblioteca responsável:
WPRO
ABSTRACT
The lupus anticoagulant-hypoprothrombinemia syndrome, characterized by presence of lupus anticoagulant with acquired factor II deficiency, is a rare disease entity often presented with acute bleeding episodes. A 15-year-old girl was hospitalized with 3 month history of menorrhagia and easy bruising. Prothrombin time (31.3 sec, normal value: 10-13 sec) and activated partial thromboplastin time (72.5 sec, normal value: 27.5-34.7 sec) were markedly prolonged and partially corrected after mixing with normal plasma. Decreased Factor II activity (4%, normal range: 79-131%) or prolonged dilute Russell's viper venom time (89.8 sec, normal value: 25.4-34.3 sec), was consistent with lupus anticoagulant-hypoprothrombinemia syndrome. Antinuclear antibody, anti-double strand-DNA antibodies and anticardiolipin antibodies were also positive. Bleeding diathesis tends to wax and wane while 5 years of treatment with steroid combined with immunosuppressants, however, there was no more active bleeding episodes. Several years after diagnosis, myocarditis, pericarditis, seizure was occurred, fulfilled the diagnostic criteria of systemic lupus erythematosus.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Tempo de Tromboplastina Parcial
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Pericardite
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Plasma
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Tempo de Protrombina
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Valores de Referência
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Convulsões
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Protrombina
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Anticorpos Antinucleares
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Inibidor de Coagulação do Lúpus
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Anticorpos Anticardiolipina
Tipo de estudo:
Diagnostic_studies
Limite:
Adolescent
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Female
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Humans
Idioma:
Ko
Revista:
Clinical Pediatric Hematology-Oncology
Ano de publicação:
2014
Tipo de documento:
Article