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Mucin-Producing Bile Duct Tumor
Journal of the Korean Surgical Society ; : 390-395, 1999.
Artigo em Coreano | WPRIM | ID: wpr-85027
ABSTRACT
BACKGROUNDS A mucin-producing bile duct tumor is a rare disease causing diffuse bile duct dilatation and intermittent obstructive jaundice due to mucin accumulation in the bile duct. A massive amount of mucin in the dilated bile duct is confirmed during surgery, endoscopic drainage, or percutaneous drainage. These tumors are usually slow-growing, well-differentiated papillary adenocarcinomas that shows intraductal spreading or an intraductal papillary growth pattern.

PURPOSE:

The purpose of this study was to evaluate the clinical, radiological, and histopathological characteristics of mucin-producing bile duct tumors.

METHODS:

We treated 10 patients with mucin-producing bile duct tumors during the recent 5 years. Clinical features were reviewed, including symptoms and signs, radiologic characteristics, operative findings, and pathological characteristics.

RESULTS:

The main clinical symptoms were recurrent abdominal pain, fever, chill, and intermittent jaundice. The characteristic radiologic findings were marked dilatation of the bile ducts distal to the tumors on computed tomography (CT) and ultrasonography and multiple, large, amorphous filling defects on cholangiography. In three cases, percutaneous transhepatic cholangioscopy (PTCS) was useful not only in making a diagnosis but also in delineating the extents of the tumors. In seven of ten cases involved (70%), the tumors were located mainly in the left intrahepatic duct. Pathologically, six (60%) cases were differentiated papillary adenocarcinoma.

CONCLUSIONS:

A mucin-producing bile duct tumor should be suspected if the patient has diffuse bile duct dilatation without definite evidence of stones, and it can be confirmed by a large amount of mucin secretion. If this type of tumor is suspected, careful preoperative evaluation, including PTCS, should be considered for making an accurate preoperative diagnosis and for determining the extent of the tumor.
Assuntos

Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Bile / Neoplasias dos Ductos Biliares / Ductos Biliares / Colangiografia / Adenocarcinoma Papilar / Dor Abdominal / Drenagem / Ultrassonografia / Doenças Raras / Icterícia Obstrutiva Tipo de estudo: Estudo diagnóstico Limite: Humanos Idioma: Coreano Revista: Journal of the Korean Surgical Society Ano de publicação: 1999 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Bile / Neoplasias dos Ductos Biliares / Ductos Biliares / Colangiografia / Adenocarcinoma Papilar / Dor Abdominal / Drenagem / Ultrassonografia / Doenças Raras / Icterícia Obstrutiva Tipo de estudo: Estudo diagnóstico Limite: Humanos Idioma: Coreano Revista: Journal of the Korean Surgical Society Ano de publicação: 1999 Tipo de documento: Artigo