Non-IgG4-Related Fibrosclerosing Periaortitis with Multisystemic Involvement / 대한내과학회지
Korean Journal of Medicine
;
: 749-754, 2014.
Artigo
em Coreano
| WPRIM
| ID: wpr-85489
ABSTRACT
Fibrosclerosing periaortitis is a rare condition that refers to a spectrum of idiopathic diseases characterized by a fibroinflammatory reaction that extends from the adventitia of the aorta into the surrounding structures. It can be present in either IgG4-related or non-IgG4-related fibrosclerosing periaortitis. IgG4-related fibrosclerosing periaortitis could be associated with concomitant multi-organ involvement. However, non-IgG4-related fibrosclerosing periaortitis has rarely been associated with systemic manifestations. Here, we report a 76-year-old female with non-IgG4-related fibrosclerosing periaortitis, who developed pancytopenia, pleural effusion and ascites, which improved after high dose steroid treatment.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Aorta
/
Pancitopenia
/
Derrame Pleural
/
Ascite
/
Fibrose Retroperitoneal
/
Imunoglobulina G
/
Túnica Adventícia
Limite:
Idoso
/
Feminino
/
Humanos
Idioma:
Coreano
Revista:
Korean Journal of Medicine
Ano de publicação:
2014
Tipo de documento:
Artigo
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