Interstitial lung disease associated with juvenile dermatomyositis / 国际儿科学杂志

ABSTRACT

Juvenile dermatomyositis is a systemic autoimmune vascular disease characterized by rash and proximal myopathy.Pulmonary complications related to this disease include interstitial lung disease, aspiration pneumonia, respiratory muscle involvement, airway involvement, pleural involvement, pulmonary hypertension and mediastinal emphysema .Interstitial lung disease is the most common pulmonary involvement in juvenile dermatomyositis, which often affects the prognosis of children.Adult myositis associated interstitial lung disease has been well described in the literature, but the description of juvenile dermatomyositis associated interstitial lung disease is still lacking.This review discusses the pathogenesis, pathological types, biological markers, diagnosis, treatment and monitoring of juvenile dermatomyositis related interstitial lung disease.