Severe juvenile dermatomyositis / 中国小儿急救医学

ABSTRACT

Juvenile dermatomyositis(JDM)is a common autoimmune inflammatory myopathy in childhood.The manifestations are specific skin lesions, chronic muscular inflammation and systemic vasculitis.The treatment was mainly glucocorticoid combined with immunosuppressive agents, the overall prognosis of JDM was better than that of adults.The key to improve the prognosis of patients is to make identification and management of severe cases.This paper introduced the clinical characteristics of severe JDM, myositis specific antibody and pulmonary imaging changes, focusing on the clinical characteristics of pulmonary lesions, examinations and treatment strategies, in order to improve the recognition and diagnosis of severe JDM.