A Case of Cytophagic Histiocytic Panniculitis Associated with Hemophagocytic Lymphohistiocytosis / 대한피부과학회지
Korean Journal of Dermatology
;
: 157-159, 2021.
Artigo
em Inglês
| WPRIM
| ID: wpr-875175
ABSTRACT
Cytophagic histiocytic panniculitis (CHP) is a rare form of panniculitis, presenting lymphohistiocytic infiltration within subcutaneous fat tissue with phagocytic histiocytes. Associated systemic symptoms includes fever, hepatosplenomegaly, lymphadenopathy, serositis, pancytopenia, hepatic abnormalities, hypertriglyceridemia, and coagulopathy, which are the features of hemophagocytic lymphohistiocytosis (HLH). The patients of CHP associated with HLH may have nonfatal acute/intermittent, or rapidly fatal clinical courses, so the prompt and accurate diagnosis with immunosuppressive treatments are significant.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Idioma:
Inglês
Revista:
Korean Journal of Dermatology
Ano de publicação:
2021
Tipo de documento:
Artigo
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