Advances in the diagnosis and treatment of dipeptidyl-peptidase-like protein 6 antibody- associated encephalitis / 中华神经科杂志
Chinese Journal of Neurology
;
(12): 424-428, 2021.
Artigo
em Chinês
| WPRIM
| ID: wpr-885439
ABSTRACT
Dipeptidyl-peptidase-like protein 6 (DPPX) antibody-associated encephalitis, mediated by DPPX antibodies in serum and/or cerebrospinal fluid, is a novel autoimmune encephalitis. It presents with multifocal and diverse neurological disorders characterized by the triad of prodromal weight loss and/or gastrointestinal symptoms (diarrhea predominately), cognitive-mental dysfunction, and central nervous system hyperexcitability. Brain magnetic resonance imaging shows non-specific abnormalities. Immunotherapy can result in clinical improvements, but the disease is prone to relapse.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Tipo de estudo:
Estudo diagnóstico
Idioma:
Chinês
Revista:
Chinese Journal of Neurology
Ano de publicação:
2021
Tipo de documento:
Artigo
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