A Case of Pulmonary Blastoma
Journal of the Korean Pediatric Society
; : 999-1005, 1994.
Article
em Ko
| WPRIM
| ID: wpr-88799
Biblioteca responsável:
WPRO
ABSTRACT
Pulmonary blastoma is a rare type of malignant lung tumor comprised of epithelial and mesenchymal elements reminiscent of fetal lung. Mesenchymal element may show various patterns of differentiation toward mature tissue, such as cartilage, smooth muscle, and bone. Rhabdomyoblastic differentiation in pulmonary blastoma is quite rare. Our case of pulmonary blastoma with rhabdomyoblastic differentiation documented by electron microscopy and immunohistochemistry. Usually it has been treated with surgery, but both chemotherapy and radiotherapy have been used against the metastatic disease, and as the adjuvant setting. A 28/12-year-old girl is described who was presented with pulmonary blastoma. She underwent surgical excision of the tumor, followed by the T2protocol, a 8 cycles of combination chemotherapy consisting of actinomycin-D, adriamycin, vincristine and cyclophosphamide with the radiation therapy to the left chest cage(180cGyx11 times). The patient has been off therapy without any evidence of relapse for 24 months. We report a case of pulmonary blastoma with brief review of related literatures.
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Radioterapia
/
Recidiva
/
Tórax
/
Vincristina
/
Imuno-Histoquímica
/
Microscopia Eletrônica
/
Cartilagem
/
Doxorrubicina
/
Blastoma Pulmonar
/
Ciclofosfamida
Tipo de estudo:
Guideline
Limite:
Female
/
Humans
Idioma:
Ko
Revista:
Journal of the Korean Pediatric Society
Ano de publicação:
1994
Tipo de documento:
Article