A Case Report of Langerhans Cell Histiocytosis of Frontal Area
Journal of the Korean Cleft Palate-Craniofacial Association
;
: 37-39, 2009.
Artigo
em Coreano
| WPRIM
| ID: wpr-9444
ABSTRACT
PURPOSE:
Langerhans cell histiocytosis is a heterogenous group of Langerhans cell proliferative disorders and includeseosinophilic granuloma, Letterer-Siwe diseases, and Hand- Schuller Christian disease. We report a case of eosinophilic granuloma on frontal area.METHODS:
A 17-year-old male presented with swelling and tenderness on Lt. frontal and periorbital area. CT and MRI showed a 33 x 25 mm sized mass that involved Lt. frontal calvarium, frontotemporal meninges, and orbital roof.RESULTS:
Total excision of the mass and adjacent soft tissue, calvarium, and orbital roof was performed. Orbital roof defect was reconstructed with absorbable plate and calvarial defect was done with outer cortex of temporal bone flap. The histology revealed proliferation of histiocytes and eosinophils. Immunologically, these histiocytic cells expressed S-100 protein and CD1a. The patient is currently taking conservative treatment.CONCLUSION:
The severity of these disease and their prognosis and treatments are various. For unifocal cranial Langerhans cell histiocytosis, complete excision is the treatment of choice. We report this case with review of literature.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Órbita
/
Prognóstico
/
Crânio
/
Osso Temporal
/
Proteínas S100
/
Histiocitose
/
Granuloma Eosinófilo
/
Histiocitose de Células de Langerhans
/
Eosinófilos
/
Osso Frontal
Tipo de estudo:
Estudo prognóstico
Limite:
Adolescente
/
Humanos
/
Masculino
Idioma:
Coreano
Revista:
Journal of the Korean Cleft Palate-Craniofacial Association
Ano de publicação:
2009
Tipo de documento:
Artigo
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