Isolated Tricuspid Regurgitation: Initial Manifestation of Cardiac Amyloidosis
The Korean Journal of Thoracic and Cardiovascular Surgery
;
: 422-425, 2015.
Artigo
em Inglês
| WPRIM
| ID: wpr-95469
ABSTRACT
Amyloid deposits in the heart are not exceptional in systemic amyloidosis. The clinical manifestations of cardiac amyloidosis may include restrictive cardiomyopathy, characterized by progressive diastolic and eventually systolic bi-ventricular dysfunction; arrhythmia; and conduction defects. To the best of our knowledge, no previous cases of isolated tricuspid regurgitation as the initial manifestation of cardiac amyloidosis have been reported. We describe a rare case of cardiac amyloidosis that initially presented with severe tricuspid regurgitation in a 42-year-old woman who was successfully treated with tricuspid valve replacement. Unusual surgical findings prompted additional evaluation that established a diagnosis of plasma cell myeloma.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Arritmias Cardíacas
/
Valva Tricúspide
/
Insuficiência da Valva Tricúspide
/
Cardiomiopatia Restritiva
/
Placa Amiloide
/
Diagnóstico
/
Coração
/
Amiloidose
/
Mieloma Múltiplo
Tipo de estudo:
Estudo diagnóstico
Limite:
Adulto
/
Feminino
/
Humanos
Idioma:
Inglês
Revista:
The Korean Journal of Thoracic and Cardiovascular Surgery
Ano de publicação:
2015
Tipo de documento:
Artigo
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