Case report of lung transplantation for cystic fibrosis in a child / 中华实用儿科临床杂志

ABSTRACT

The clinical and genetic data of a child with cystic fibrosis who received double lung transplantation were retrospectively analyzed and related problems of cystic fibrosis lung transplantation were discussed.The child was diagnosed with cystic fibrosis in the Department of Respiratory, the Affiliated Children′s Hospital of Capital Institute of Pediatrics at the age of 6 years for the first time.The patient was hospitalized repeatedly for exacerbation of pulmonary infection, with no significant clinical improvement and progressive aggravation of malnutrition.In October 2019, the patient received double lung transplantation at the age of 17 years and 1 month.Two years after surgery, the clinical symptoms and quality of life have been notably improved, and no transplant-related complications were observed.Lung transplantation is an effective treatment for children with advanced cystic fibrosis lung disease.