Pulmonary alveolar proteinosis in a 15-year-old girl
Allergy, Asthma & Respiratory Disease
;
: 86-89, 2015.
Artigo
em Coreano
| WPRIM
| ID: wpr-99816
ABSTRACT
Pulmonary alveolar proteinosis (PAP) is a diffuse lung disease characterized by the accumulation of lipoproteins derived from surfactants in the distal air space. The lack of granulocyte macrophage colony-stimulating factor is believed to contribute to macrophage dysfunction and the impaired processing of surfactants. Because the prevalence of PAP in the general population is less than 1 in 200,000, and the typical age at presentation is 35 to 50 years, PAP is a very rare disease in children. To the best of our knowledge, there has been no Korean report on PAP in children. We describe here a patient who was diagnosed with PAP at the aged 15 years.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Proteinose Alveolar Pulmonar
/
Tensoativos
/
Prevalência
/
Fator Estimulador de Colônias de Macrófagos
/
Doenças Raras
/
Granulócitos
/
Lipoproteínas
/
Pneumopatias
/
Macrófagos
Tipo de estudo:
Estudo de prevalência
Limite:
Adolescente
/
Criança
/
Feminino
/
Humanos
Idioma:
Coreano
Revista:
Allergy, Asthma & Respiratory Disease
Ano de publicação:
2015
Tipo de documento:
Artigo
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