Proceedings of the 27th European Paediatric Rheumatology Congress (PReS 2021) : Virtual. 19-21 September 2021

ABSTRACT

The proceedings contain 431 papers. The topics discussed include long-term efficacy and safety of canakinumab in patients with mevalonate kinase deficiency results from the randomized phase 3 cluster trial;long-term safety of canakinumab in patients with autoinflammatory periodic fever syndromes - interim analysis of the reliance registry;NLRP3 splice variants inactivate caps phenotype in vitro;OAS1 GOF causes a novel autoinflammatory disease characterized by persistently elevated ifn signature, hypogammaglobulinemia, and alveolar proteinosis;while looking for one, you may find another tin soldiers and the search for undiagnosed individuals with fibrodysplasia ossificans progressiva (FOP);nailfold capillaroscopy a sensitive method for evaluating microvascular involvement in children with SARS-COV-2 infection;and outcomes of COVID-19 infection among children and young people with pre-existing rheumatic and musculoskeletal diseases.