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Giant Aortic Aneurysm in Child with Cutis Laxa Syndrome: Unusual Presentation, New Surgical Technique.
Shamsaldeen Faden, Mazen; Ahmed Noaman, Nada; Osman Osama, Osman Osama; Elassal, Ahmed Abdelrahman; Al-Ghamdi, Arwa Mohammed; Debis, Ragab.
  • Shamsaldeen Faden M; 1Department of Anesthesia and Critical Care, King Abdul-Aziz University Hospital, Jeddah, Kingdom Saudi Arabia;. Openheart32@gmail.com.
  • Ahmed Noaman N; 1Department of Anesthesia and Critical Care, King Abdul-Aziz University Hospital, Jeddah, Kingdom Saudi Arabia;. Openheart32@gmail.com.
  • Osman Osama OO; Department of Surgery, Cardiac Surgery Unit, King Abdul-Aziz University, Jeddah, Saudi Arabia. Openheart32@gmail.com.
  • Elassal AA; Cardiothoracic Surgery Department, Zagazig University, Zagazig, Egypt. Openheart32@gmail.com.
  • Al-Ghamdi AM; Cardiac Surgery Unit, Co-ordination Unit, King Abdul-Aziz University, Jeddah, Saudi Arabia. Openheart32@gmail.com.
  • Debis R; 1Department of Anesthesia and Critical Care, King Abdul-Aziz University Hospital, Jeddah, Kingdom Saudi Arabia;. openheart32@gmail.com.
Heart Surg Forum ; 24(6): E1054-E1056, 2021 Dec 17.
Article in English | MEDLINE | ID: covidwho-1597972
ABSTRACT
Ascending thoracic aortic aneurysms are rare in childhood and typically are seen in the setting of connective tissue defect syndromes. These aneurysms may lead to rupture, dissection, or valvular insufficiency, so root replacement is recommended. Here, we present a 17-month-old girl who presented with fever, cough, and pericardial effusion. Initially, we suspected this could be a COVID-19 case, so a nasopharyngeal swap was performed. An ascending aorta aneurysm involving the aortic arch was confirmed by echo, and urgent ascending aorta and arch replacement were done by utilizing the descending aorta as a new arch. The final diagnosis came with cutis laxa syndrome. In similar cases, good outcomes can be achieved with accurate diagnosis and appropriate surgical management.
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Full text: Available Collection: International databases Database: MEDLINE Main subject: Aorta, Thoracic / Aortic Aneurysm / Cutis Laxa Type of study: Case report / Diagnostic study / Observational study / Randomized controlled trials Topics: Long Covid Limits: Female / Humans / Infant Language: English Journal: Heart Surg Forum Journal subject: Cardiology Year: 2021 Document Type: Article

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Full text: Available Collection: International databases Database: MEDLINE Main subject: Aorta, Thoracic / Aortic Aneurysm / Cutis Laxa Type of study: Case report / Diagnostic study / Observational study / Randomized controlled trials Topics: Long Covid Limits: Female / Humans / Infant Language: English Journal: Heart Surg Forum Journal subject: Cardiology Year: 2021 Document Type: Article