Giant Aortic Aneurysm in Child with Cutis Laxa Syndrome: Unusual Presentation, New Surgical Technique.
Heart Surg Forum
; 24(6): E1054-E1056, 2021 Dec 17.
Article
in English
| MEDLINE | ID: covidwho-1597972
ABSTRACT
Ascending thoracic aortic aneurysms are rare in childhood and typically are seen in the setting of connective tissue defect syndromes. These aneurysms may lead to rupture, dissection, or valvular insufficiency, so root replacement is recommended. Here, we present a 17-month-old girl who presented with fever, cough, and pericardial effusion. Initially, we suspected this could be a COVID-19 case, so a nasopharyngeal swap was performed. An ascending aorta aneurysm involving the aortic arch was confirmed by echo, and urgent ascending aorta and arch replacement were done by utilizing the descending aorta as a new arch. The final diagnosis came with cutis laxa syndrome. In similar cases, good outcomes can be achieved with accurate diagnosis and appropriate surgical management.
Full text:
Available
Collection:
International databases
Database:
MEDLINE
Main subject:
Aorta, Thoracic
/
Aortic Aneurysm
/
Cutis Laxa
Type of study:
Case report
/
Diagnostic study
/
Observational study
/
Randomized controlled trials
Topics:
Long Covid
Limits:
Female
/
Humans
/
Infant
Language:
English
Journal:
Heart Surg Forum
Journal subject:
Cardiology
Year:
2021
Document Type:
Article
Similar
MEDLINE
...
LILACS
LIS