Spectrum of Large- and Medium-Vessel Vasculitis in Adults: Neoplastic, Infectious, Drug-Induced, Autoinflammatory, and Primary Immunodeficiency Diseases.
Curr Rheumatol Rep
; 24(10): 293-309, 2022 10.
Article
in English
| MEDLINE | ID: covidwho-2060051
ABSTRACT
PURPOSE OF REVIEW To provide a comprehensive review of drugs and neoplastic, infectious, autoinflammatory, and immunodeficiency diseases causing medium- to large-vessel vasculitis in adults with emphasis on information essential for the initial diagnostic process. RECENT FINDINGS:
Entities with medium- to large-vessel vasculitis as clinical manifestations have been described recently (e.g., adenosine deaminase-2 deficiency, VEXAS-Syndrome), and vasculitis in established autoinflammatory or immunodeficiency diseases is increasingly being identified. In the diagnostic process of medium- to large-vessel vasculitis in adults, a large variety of rare diseases should be included in the differential diagnosis, especially if diagnosis is made without histologic confirmation and in younger patients. Although these disorders should be considered, they will undoubtedly remain rare in daily practice.Keywords
Full text:
Available
Collection:
International databases
Database:
MEDLINE
Main subject:
Polyarteritis Nodosa
/
Vasculitis
/
Primary Immunodeficiency Diseases
Type of study:
Diagnostic study
/
Prognostic study
Limits:
Adult
/
Humans
Language:
English
Journal:
Curr Rheumatol Rep
Journal subject:
Rheumatology
Year:
2022
Document Type:
Article
Affiliation country:
S11926-022-01083-5
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