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Spectrum of Large- and Medium-Vessel Vasculitis in Adults: Neoplastic, Infectious, Drug-Induced, Autoinflammatory, and Primary Immunodeficiency Diseases.
Lötscher, Fabian; Pop, Roxana; Seitz, Pascal; Recher, Mike; Seitz, Luca.
  • Lötscher F; Department of Rheumatology and Immunology, Inselspital, University Hospital, University of Bern, Freiburgstrasse, CH-3010, Bern, Switzerland.
  • Pop R; Department of Infectious Diseases and Hospital Hygiene, University Hospital, University of Zurich, Zurich, Switzerland.
  • Seitz P; Department of Rheumatology and Immunology, Inselspital, University Hospital, University of Bern, Freiburgstrasse, CH-3010, Bern, Switzerland.
  • Recher M; Immunodeficiency Laboratory, Department of Biomedicine, University Hospital and University of Basel, Basel, Switzerland.
  • Seitz L; University Center for Immunology, University Hospital, Basel, Switzerland.
Curr Rheumatol Rep ; 24(10): 293-309, 2022 10.
Article in English | MEDLINE | ID: covidwho-2060051
ABSTRACT
PURPOSE OF REVIEW To provide a comprehensive review of drugs and neoplastic, infectious, autoinflammatory, and immunodeficiency diseases causing medium- to large-vessel vasculitis in adults with emphasis on information essential for the initial diagnostic process. RECENT

FINDINGS:

Entities with medium- to large-vessel vasculitis as clinical manifestations have been described recently (e.g., adenosine deaminase-2 deficiency, VEXAS-Syndrome), and vasculitis in established autoinflammatory or immunodeficiency diseases is increasingly being identified. In the diagnostic process of medium- to large-vessel vasculitis in adults, a large variety of rare diseases should be included in the differential diagnosis, especially if diagnosis is made without histologic confirmation and in younger patients. Although these disorders should be considered, they will undoubtedly remain rare in daily practice.
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Full text: Available Collection: International databases Database: MEDLINE Main subject: Polyarteritis Nodosa / Vasculitis / Primary Immunodeficiency Diseases Type of study: Diagnostic study / Prognostic study Limits: Adult / Humans Language: English Journal: Curr Rheumatol Rep Journal subject: Rheumatology Year: 2022 Document Type: Article Affiliation country: S11926-022-01083-5

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Full text: Available Collection: International databases Database: MEDLINE Main subject: Polyarteritis Nodosa / Vasculitis / Primary Immunodeficiency Diseases Type of study: Diagnostic study / Prognostic study Limits: Adult / Humans Language: English Journal: Curr Rheumatol Rep Journal subject: Rheumatology Year: 2022 Document Type: Article Affiliation country: S11926-022-01083-5