Dorsal pancreatic agenesis: Case report and topic review

ABSTRACT

Complete agenesis of the dorsal pancreas (ADP) is an exceedingly rare congenital anomaly, compatible with life. It is frequently asymptomatic and usually incidentally diagnosed. In symptomatic cases, the clinical manifestations vary from abdominal pain, pancreatitis and diabetes mellitus to exocrine insufficiency with steatorrhea. We present a case report of a 28-year-old female with ADP, diagnosed incidentally during radiological evaluation for hyperglycemias during a SARS-CoV2 concomitant infection. Magnetic resonance cholangiopancreatography confirmed the absence of neck, body and tail of the pancreas. Familiarization with pancreatic embryogenesis, as well as the clinical presentation and main radiological characteristics of its anomalies is important for the proper diagnosis of these malformations.