A rare case of Rosai-Dorfman disease presenting as a pulmonary artery mass in a 33-year-old female with hypoxia.
Pulm Circ
; 13(2): e12214, 2023 Apr.
Article
in English
| MEDLINE | ID: covidwho-2257630
ABSTRACT
Rosai-Dorfman disease (RDD) is a rare form of non-Langerhans histiocytosis. It is often idiopathic in etiology, but has been associated with viral, autoimmune, and malignant disease. Adequate diagnosis of RDD requires a combination of clinical symptoms, radiography, and histology. Most commonly, patients with RDD present with cervical lymphadenopathy. We describe a case of a young female who was initially thought to have a pulmonary embolism at the time of a COVID-19 infection but was noted to have a rare occurrence of RDD presenting as a pulmonary artery mass upon further evaluation of radiology and histology. Though RDD is frequently benign, extranodal involvement can progress to end organ damage and must be recognized appropriately.
Full text:
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Collection:
International databases
Database:
MEDLINE
Type of study:
Case report
/
Etiology study
/
Experimental Studies
/
Prognostic study
Language:
English
Journal:
Pulm Circ
Year:
2023
Document Type:
Article
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