Highlights of the Management of Adult Histiocytic Disorders: Langerhans Cell Histiocytosis, Erdheim-Chester Disease, Rosai-Dorfman Disease, and Hemophagocytic Lymphohistiocytosis.
Clin Lymphoma Myeloma Leuk
; 21(1): e66-e75, 2021 01.
Article
in English
| MEDLINE | ID: covidwho-718689
ABSTRACT
Histiocytic disorders are an exceptionally rare group of diseases with diverse manifestations and a paucity of approved treatments, thereby leading to various challenges in their diagnosis and management. With the discovery of novel molecular targets and the incorporation of targeted agents in the management of various adult histiocytic disorders, their management has become increasingly complex. In an attempt to improve the understanding of the clinical features and management of common adult histiocytic disorders (Langerhans cell histiocytosis, Erdheim-Chester disease, Rosai-Dorfman disease, and hemophagocytic lymphohistiocytosis), we created this document based on existing literature and expert opinion.
Keywords
Full text:
Available
Collection:
International databases
Database:
MEDLINE
Main subject:
Histiocytosis, Sinus
/
Histiocytosis, Langerhans-Cell
/
Erdheim-Chester Disease
/
Lymphohistiocytosis, Hemophagocytic
Type of study:
Diagnostic study
/
Prognostic study
Limits:
Adult
/
Humans
Language:
English
Journal:
Clin Lymphoma Myeloma Leuk
Journal subject:
Neoplasms
Year:
2021
Document Type:
Article
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