Detalles de la búsqueda
1.
Underlying molecular alterations in human dihydrolipoamide dehydrogenase deficiency revealed by structural analyses of disease-causing enzyme variants.
Hum Mol Genet
; 28(20): 3339-3354, 2019 10 15.
Artículo
en Inglés
| MEDLINE | ID: mdl-31334547
2.
Reduction of 2-methoxy-1,4-naphtoquinone by mitochondrially-localized Nqo1 yielding NAD+ supports substrate-level phosphorylation during respiratory inhibition.
Biochim Biophys Acta Bioenerg
; 1859(9): 909-924, 2018 09.
Artículo
en Inglés
| MEDLINE | ID: mdl-29746824
3.
Structural alterations induced by ten disease-causing mutations of human dihydrolipoamide dehydrogenase analyzed by hydrogen/deuterium-exchange mass spectrometry: Implications for the structural basis of E3 deficiency.
Biochim Biophys Acta
; 1862(11): 2098-2109, 2016 Nov.
Artículo
en Inglés
| MEDLINE | ID: mdl-27544700
4.
The total and mitochondrial lipidome of Artemia franciscana encysted embryos.
Biochim Biophys Acta
; 1861(11): 1727-1735, 2016 11.
Artículo
en Inglés
| MEDLINE | ID: mdl-27542539
5.
Abolition of mitochondrial substrate-level phosphorylation by itaconic acid produced by LPS-induced Irg1 expression in cells of murine macrophage lineage.
FASEB J
; 30(1): 286-300, 2016 Jan.
Artículo
en Inglés
| MEDLINE | ID: mdl-26358042
6.
Two transgenic mouse models for ß-subunit components of succinate-CoA ligase yielding pleiotropic metabolic alterations.
Biochem J
; 473(20): 3463-3485, 2016 10 15.
Artículo
en Inglés
| MEDLINE | ID: mdl-27496549
7.
Human 2-oxoglutarate dehydrogenase complex E1 component forms a thiamin-derived radical by aerobic oxidation of the enamine intermediate.
J Biol Chem
; 289(43): 29859-73, 2014 Oct 24.
Artículo
en Inglés
| MEDLINE | ID: mdl-25210035
8.
Localization of SUCLA2 and SUCLG2 subunits of succinyl CoA ligase within the cerebral cortex suggests the absence of matrix substrate-level phosphorylation in glial cells of the human brain.
J Bioenerg Biomembr
; 47(1-2): 33-41, 2015 Apr.
Artículo
en Inglés
| MEDLINE | ID: mdl-25370487
9.
Mitochondrial diaphorases as NAD⺠donors to segments of the citric acid cycle that support substrate-level phosphorylation yielding ATP during respiratory inhibition.
FASEB J
; 28(4): 1682-97, 2014 Apr.
Artículo
en Inglés
| MEDLINE | ID: mdl-24391134
10.
The negative impact of α-ketoglutarate dehydrogenase complex deficiency on matrix substrate-level phosphorylation.
FASEB J
; 27(6): 2392-406, 2013 Jun.
Artículo
en Inglés
| MEDLINE | ID: mdl-23475850
11.
Stimulation of reactive oxygen species generation by disease-causing mutations of lipoamide dehydrogenase.
Hum Mol Genet
; 20(15): 2984-95, 2011 Aug 01.
Artículo
en Inglés
| MEDLINE | ID: mdl-21558426
12.
Molecular dynamics study of the structural basis of dysfunction and the modulation of reactive oxygen species generation by pathogenic mutants of human dihydrolipoamide dehydrogenase.
Arch Biochem Biophys
; 538(2): 145-55, 2013 Oct 15.
Artículo
en Inglés
| MEDLINE | ID: mdl-24012808
13.
Complex contribution of cyclophilin D to Ca2+-induced permeability transition in brain mitochondria, with relation to the bioenergetic state.
J Biol Chem
; 286(8): 6345-53, 2011 Feb 25.
Artículo
en Inglés
| MEDLINE | ID: mdl-21173147
14.
Mitochondria as ATP consumers in cellular pathology.
Biochim Biophys Acta
; 1802(1): 221-7, 2010 Jan.
Artículo
en Inglés
| MEDLINE | ID: mdl-19715757
15.
Membrane potential-related effect of calcium on reactive oxygen species generation in isolated brain mitochondria.
Biochim Biophys Acta
; 1797(6-7): 922-8, 2010.
Artículo
en Inglés
| MEDLINE | ID: mdl-20230776
16.
Reversible inhibition of hydrogen peroxide elimination by calcium in brain mitochondria.
J Neurosci Res
; 89(12): 1965-72, 2011 Dec.
Artículo
en Inglés
| MEDLINE | ID: mdl-21541982
17.
Forward operation of adenine nucleotide translocase during F0F1-ATPase reversal: critical role of matrix substrate-level phosphorylation.
FASEB J
; 24(7): 2405-16, 2010 Jul.
Artículo
en Inglés
| MEDLINE | ID: mdl-20207940
18.
Structure of the dihydrolipoamide succinyltransferase (E2) component of the human alpha-ketoglutarate dehydrogenase complex (hKGDHc) revealed by cryo-EM and cross-linking mass spectrometry: Implications for the overall hKGDHc structure.
Biochim Biophys Acta Gen Subj
; 1865(6): 129889, 2021 06.
Artículo
en Inglés
| MEDLINE | ID: mdl-33684457
19.
Exclusive neuronal detection of KGDHC-specific subunits in the adult human brain cortex despite pancellular protein lysine succinylation.
Brain Struct Funct
; 225(2): 639-667, 2020 Mar.
Artículo
en Inglés
| MEDLINE | ID: mdl-31982949
20.
A novel kinetic assay of mitochondrial ATP-ADP exchange rate mediated by the ANT.
Biophys J
; 96(6): 2490-504, 2009 Mar 18.
Artículo
en Inglés
| MEDLINE | ID: mdl-19289073