Detalles de la búsqueda
1.
Protective effects of L-carnitine on behavioral alterations and neuroinflammation in striatum of glutaryl-COA dehydrogenase deficient mice.
Arch Biochem Biophys
; 709: 108970, 2021 09 30.
Artículo
en Inglés
| MEDLINE | ID: mdl-34181873
2.
Higher susceptibility of cerebral cortex and striatum to sulfite neurotoxicity in sulfite oxidase-deficient rats.
Biochim Biophys Acta
; 1862(11): 2063-2074, 2016 Nov.
Artículo
en Inglés
| MEDLINE | ID: mdl-27523630
3.
Bezafibrate prevents mitochondrial dysfunction, antioxidant system disturbance, glial reactivity and neuronal damage induced by sulfite administration in striatum of rats: Implications for a possible therapeutic strategy for sulfite oxidase deficiency.
Biochim Biophys Acta Mol Basis Dis
; 1863(9): 2135-2148, 2017 09.
Artículo
en Inglés
| MEDLINE | ID: mdl-28529047
4.
Evidence that glycine induces lipid peroxidation and decreases glutathione concentrations in rat cerebellum.
Mol Cell Biochem
; 395(1-2): 125-34, 2014 Oct.
Artículo
en Inglés
| MEDLINE | ID: mdl-24939360
5.
Neurochemical evidence that the metabolites accumulating in 3-methylcrotonyl-CoA carboxylase deficiency induce oxidative damage in cerebral cortex of young rats.
Cell Mol Neurobiol
; 33(1): 137-46, 2013 Jan.
Artículo
en Inglés
| MEDLINE | ID: mdl-23053545
6.
Experimental evidence that pristanic acid disrupts mitochondrial homeostasis in brain of young rats.
J Neurosci Res
; 90(3): 597-605, 2012 Mar.
Artículo
en Inglés
| MEDLINE | ID: mdl-22183871
7.
3-Methylcrotonylglycine disrupts mitochondrial energy homeostasis and inhibits synaptic Na(+),K (+)-ATPase activity in brain of young rats.
Cell Mol Neurobiol
; 32(2): 297-307, 2012 Mar.
Artículo
en Inglés
| MEDLINE | ID: mdl-21993987
8.
Phytanic acid disturbs mitochondrial homeostasis in heart of young rats: a possible pathomechanism of cardiomyopathy in Refsum disease.
Mol Cell Biochem
; 366(1-2): 335-43, 2012 Jul.
Artículo
en Inglés
| MEDLINE | ID: mdl-22527938
9.
Chronic postnatal ornithine administration to rats provokes learning deficit in the open field task.
Metab Brain Dis
; 27(4): 479-86, 2012 Dec.
Artículo
en Inglés
| MEDLINE | ID: mdl-22699997
10.
Impairment of brain redox homeostasis caused by the major metabolites accumulating in hyperornithinemia-hyperammonemia-homocitrullinuria syndrome in vivo.
Metab Brain Dis
; 27(4): 521-30, 2012 Dec.
Artículo
en Inglés
| MEDLINE | ID: mdl-22798168
11.
Neurochemical evidence that pristanic acid impairs energy production and inhibits synaptic Na(+), K(+)-ATPase activity in brain of young rats.
Neurochem Res
; 36(6): 1101-7, 2011 Jun.
Artículo
en Inglés
| MEDLINE | ID: mdl-21445584
12.
Promotion of lipid and protein oxidative damage in rat brain by ethylmalonic acid.
Neurochem Res
; 35(2): 298-305, 2010 Feb.
Artículo
en Inglés
| MEDLINE | ID: mdl-19757035
13.
Investigation of correlation of urinary globotriaosylceramide (Gb3) levels with markers of renal function in patients with Fabry disease.
Clin Chim Acta
; 478: 62-67, 2018 Mar.
Artículo
en Inglés
| MEDLINE | ID: mdl-29274327
14.
Evidence that Thiosulfate Inhibits Creatine Kinase Activity in Rat Striatum via Thiol Group Oxidation.
Neurotox Res
; 34(3): 693-705, 2018 Oct.
Artículo
en Inglés
| MEDLINE | ID: mdl-30056533
15.
Glycine Administration Alters MAPK Signaling Pathways and Causes Neuronal Damage in Rat Brain: Putative Mechanisms Involved in the Neurological Dysfunction in Nonketotic Hyperglycinemia.
Mol Neurobiol
; 55(1): 741-750, 2018 01.
Artículo
en Inglés
| MEDLINE | ID: mdl-28050793
16.
Intracerebral Glycine Administration Impairs Energy and Redox Homeostasis and Induces Glial Reactivity in Cerebral Cortex of Newborn Rats.
Mol Neurobiol
; 53(9): 5864-5875, 2016 11.
Artículo
en Inglés
| MEDLINE | ID: mdl-26497039
17.
In vitro evidence that sulfite impairs glutamatergic neurotransmission and inhibits glutathione metabolism-related enzymes in rat cerebral cortex.
Int J Dev Neurosci
; 42: 68-75, 2015 May.
Artículo
en Inglés
| MEDLINE | ID: mdl-25777939
18.
Disturbance of brain energy and redox homeostasis provoked by sulfite and thiosulfate: potential pathomechanisms involved in the neuropathology of sulfite oxidase deficiency.
Gene
; 531(2): 191-8, 2013 Dec 01.
Artículo
en Inglés
| MEDLINE | ID: mdl-24035933
19.
Disturbance of redox homeostasis by ornithine and homocitrulline in rat cerebellum: a possible mechanism of cerebellar dysfunction in HHH syndrome.
Life Sci
; 93(4): 161-8, 2013 Aug 06.
Artículo
en Inglés
| MEDLINE | ID: mdl-23806752
20.
Glycine intracerebroventricular administration disrupts mitochondrial energy homeostasis in cerebral cortex and striatum of young rats.
Neurotox Res
; 24(4): 502-11, 2013 Nov.
Artículo
en Inglés
| MEDLINE | ID: mdl-23640702