Abstract
Dermatitis herpetiformis and
linear IgA bullous dermatosis are
autoimmune diseases that present with pruritic urticarial papules and plaques, with formation of vesicles and
blisters of subepidermal
location , mediated by
IgA antibodies . Mucosal lesions are present only in
linear IgA bullous dermatosis . The elaboration of this
consensus consisted of a brief presentation of the different aspects of these
dermatoses and, above all, of an updated
literature review on the various
therapeutic options that were discussed and compared with the authors' experience, aiming at the
treatment orientation of these
diseases in
Brazil .
Dermatitis herpetiformis is a cutaneous manifestation of
celiac disease , and can be controlled with a
gluten-free diet and
dapsone . On the other
hand ,
linear IgA bullous dermatosis arises spontaneously or is triggered by
drugs , and can be controlled with
dapsone , but often requires the
association of systemic
corticosteroids and eventually
immunosuppressants .