Registry of transthyretin amyloidosis in the state of São Paulo (REACT-SP) / Registro em amiloidose transtirretina do estado de São Paulo (REACT-SP)
Fernandes, Fabio; Cafezeiro, Caio; Margarida do Val, Renata; Vieira, Alexandra Patrícia Zilli; Marques, Wilson; Correia, Edileide Barros; Carvalho, Alzira Alves Siqueira; Chagas, Antonio Carlos Palandrini; Oliveira, Acary Souza Bulle; Souza, Paulo Victor Sgobi de; Pinto, Wladimir Bocca Vieira de Resende; Macedo, Ariane Vieira Scarlatelli; Antunes, Murillo Oliveira; Schwartzmann, Pedro Vellosa; Mangini, Sandrigo; Simões, Marcus Vinicius.
ABC Heart Fail Cardiomyop
; 1(2): 86-89, Sept. 2021. tab
Artículo
en Inglés, Portugués
| CONASS, SES-SP, SESSP-IDPCPROD, SES-SP | ID: biblio-1401854
BACKGROUND:
Amyloidosis is a systemic disease that involves multiple organs, characterized by the deposition of amyloid fibrils. Knowledge regarding the epidemiological, clinical, and genetic profile of the population affected by amyloidosis throughout the country is of fundamental importance for establishing diagnostic and therapeutic strategies.OBJECTIVE:
To evaluate the epidemiological, clinical, laboratory, imaging, and treatment variables of patients with TTR cardiac amyloidosis. MATERIALS ANDMETHODS:
A multicenter, retrospective, prospective, and observational study based on collection of data on the natural history of patients with TTR amyloidosis, followed in the state of São Paulo.RESULTS:
To make it possible to map the regional distribution of the disease, increasing knowledge about the disease among clinicians and specialists in different areas. To evaluate patients with hereditary and wild-type TTR amyloidosis, in addition to following individuals with positive genotype and negative phenotype.
Biblioteca responsable:
BR79.1
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