Epithelioid hemangioendothelioma is a multifocal
tumor that rarely metastasizes. It is difficult to
diagnose, most often it is an
incidental finding in young asymptomatic
women. The radiologic pattern is heterogeneous. Histologic confirmation of
Weibel-Palade bodies or
immunohistochemistry based on specific
tumor markers such as
factor VIII and CD34 are the most important finding to confirm the
diagnosis. We
report a 21 years old
woman Presenting with
cough and
dyspnea. A
chest X ray was suggestive of
tuberculosis.
Sputum smears were negative for
acid fat bacilli and the
tuberculin test was negative. A
chest CAT scan showed multiple nodular lesions. A surgical
biopsy of the lesions confirmed the presence of a
hemangioendothelioma. The
patient was initially treated with
prednisone and
azathioprine without response. Thereafter, the
patient is without
treatment and without evidence of
disease progression.