Rasmussen syndrome or
Rasmussen encephalitis is a rare, progressive
gray matter disease of childhood. A case of 4-year-old boy is reported here,
who presented with recurrent episodes of
status epilepticus of simple partial fits along with progressive left sided
hemiplegia.
EEG showed focal discharges from right hemisphere. Serial MRI
brain showed progressive
atrophy of
right cerebral hemisphere with
dilatation of ipsilateral ventricle