Variante faringo-cérvico-braquial da síndrome de Guillain-Barré:uma causa rara de disfunção bulbar aguda em crianças / Pharyngeal-cervical-brachial variant of Guillain-Barré syndrome:a rare cause of acute bulbar dysfunction in children
Coelho, Joana; Azevedo, Sara; Abecasis, Francisco; Furtado, Fátima; Quintas, Sofia; Levy, António.
Sci. med
; 24(4): 381-384, out-dez.2014.
Artículo
en Inglés
|
LILACS-Express
| ID: lil-747230
Aims:
To report a case of pharyngeal-cervical-brachial variant of Guillain-Barré syndrome, which is characterized by rapidly progressivebulbar palsy with upper limb, neck and oropharyngeal involvement. It is a rare disorder in childhood and most cases have been described inadolescents.Case Description A seven year-old-boy presented with dysarthria, hoarseness, dysphagia, facial diplegia and bilateral progressive upperlimb weakness. These symptoms started two weeks after a gastrointestinal infection. Nerve conduction studies were compatible with an acutedemyelinating polyneuropathy in the upper extremities. Anti-ganglioside antibodies in the serum (anti-GT1a, GD1a, GQ1b) were positiveand Campylobacter jejuni was isolated from stools. The patient was treated with intravenous immunoglobulin and needed ventilatory supportduring the first 12 days of admission. He was discharged at day 15 showing improvement of his neurological deficits. He fully recovered aftereleven months of follow-up.Conclusions:
Although pharyngeal-cervical-brachial variant of Guillain-Barré syndrome is uncommon in children, it should be consideredin a child with acute bulbar dysfunction because a timely diagnosis allows the early institution of therapeutic measures that can be lifesaving.
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