Achalasia is an uncommon disorder that affects about 1 in every 100,000 people. The major symptom of achalasia is usually difficulty with swallowing. Other symptoms can include chest pain, regurgitation, bronchoaspiration pneumonia and weight loss. Most people are diagnosed between the ages of 25 and 60 years. May be suspected based upon symptoms, but tests are needed to confirm the diagnosis. Manometry is almost always used to confirm the diagnosis of achalasia. We report a case with patient with atypical presentation of disease where the lack of diagnosis affected the quality of life.