Background:
Calcinosis cutis is usually seen in long standing and untreated cases of
juvenile dermatomyositis. Case characteristics 7-year-old
girl with severe
calcinosis cutis who developed cutaneous ulceration,
rash and
myopathy.
Observation Myopathic changes in EMG,
muscle edema in MRI, elevated
muscle enzymes and Jo-1 positive
antibodies.
Outcome:
Treatment with
prednisolone and
methotrexate resulted in improvement of the lesion. Message
Calcinosis cutis may be a presenting feature of
juvenile dermatomyositis even in the absence of characteristic findings of
rash and weakness.