Biblioteca Virtual en Salud

Amelogenesis imperfecta is a developmental disorder which affects enamel. This developmental defect leads to weakening of the enamel leading to an overall discolouration, pitting erosion of the enamel, white hypoplastic spots and multiple carious lesions. A 23-year-old patient came to the Department of Prosthodontics with a chief complaint of aesthetic correction of her teeth. She requested an immediate solution to her problem. She was diagnosed as a case of Hypoplastic Amelogenesis Imperfecta. She showed a strong familial history for this genetic disorder. A digitally driven protocol for full mouth rehabilitation was planned for her to facilitate ease and precision with faster results in a short period of time. Digitally milled all ceramic restorations were planned for marginal accuracy and final results. This hypoplastic variety of AI showed the maximum longevity of dental restorations compared to the other types. This case report elaborates on a combination of conventional and digital rehabilitation of a patient with a hypoplastic type of Amelogenesis Imperfecta.Amelogenesis Imperfecta is a rare hereditary disorder which causes structural abnormalities in the enamel.1 It is a sex linked genetic disorder with either maternal or paternal descent.1,2 There are 3 forms of Amelogenesis Imperfecta - Hypoplastic, Hypocalcific, and Hypomaturation.3 The characteristics of this disorder are the loss of tooth structure especially enamel, weakened enamel lead to pitting erosion, yellowish brown discolouration, tendency for multiple carious lesions, dentinal hypersensitivity.4 This can also lead to the excessive and faster wear of enamel at a young age leading to loss of vertical dimension.5 The paternal or maternal family history gives the children a 50 % chance of getting this disorder.The severity of this disorder varies according to its different types. The most commonly occurring Amelogenesis Imperfecta is the Hypoplastic type.6 Around 61 % of the patients have Hypoplastic type of AI. There are multiple variations also seen in this type of Amelogenesis Imperfecta.7 This type has the maximum longevity of the dental restorations compared to the other types of Amelogenesis Imperfecta.8 Patients with this disorder have a very low morale and confidence in the society.9 This leads to social awkwardness and inability to openly smile or laugh. These patients must be handled with utmost care and emotions.10 In this case report, we are going to explain a full mouth rehabilitation protocol with a combination of conventional and digital techniques to achieve a stable result functionally and aesthetically.