Hepatic
angiosarcoma (HAS) is an extremely rare
liver tumor in
children. We
report a case of childhood HAS in a six year old
girl who presented with acute
abdominal pain and
fever with a mass in epigastrium. Left hepatic lobectomy was performed with a
clinical diagnosis of
hepatoblastoma. Histopathological examination revealed features typical of hepatic
angiosarcoma. The case is presented for its rarity and to discuss the interrelation between infantile
hemangioendothelioma (IHE) and HAS.