The
incidence of
horseshoe kidney is about 1 in 400 cases. The presence of
Wilms' tumor with a
horseshoe kidney is unusual, and the occurrence of
Wilms' tumor in a
horseshoe kidney is estimated at 0.4 to 0.9% of all Wilms'
tumors. We
report the case of a 5-year-old boy
who presented with a stage IV
Wilms' tumor in a
horseshoe kidney. The
patient was treated with preoperative
chemotherapy followed by surgical resection and
adjuvant chemotherapy. This case illustrates the
role of preoperative
chemotherapy for preserving renal function and aims to highlight the multimodality
treatment of
Wilms' tumor.