A
congenital cholesteatoma is a benign mass formed from the keratinizing stratified squamous
epithelium. It usually occurs in young
children's anterosuperior part of the
middle ear. A
congenital cholesteatoma which originates from
mastoid temporal bone or expands to
posterior cranial fossa is rare. Standard
treatment of an intracranial
cholesteatoma is surgical removal with
craniotomy. A 69-year-old
woman was diagnosed with a
congenital cholesteatoma of
mastoid temporal bone that expanded to the
posterior cranial fossa, which was successfully treated with transmastoid marsupialization without
craniotomy. This is a first documented case of a
congenital cholesteatoma of
mastoid temporal bone that expanded to
posterior cranial fossa, which was successfully treated with transmastoid marsupialization without
craniotomy.