Immunoglobulin G4-related disease is a recently recognized entity characterized by a mass-forming or regional lesion that contains an extensive infiltration of
IgG4-producing
plasma cells with dense
fibrosis.
Immunoglobulin G4-related disease can
affect any organ system, but solitary hepatic lesion of
Immunoglobulin G4-related disease is very rare. This entity mimics primary malignant hepatic
tumor, such as
hepatocellular carcinoma or
intrahepatic cholangiocarcinoma. We experienced a case of hepatic
IgG4-related
inflammatory pseudotumor in a 50-year-old
woman, mimicking
hepatocellular carcinoma.