Chronic inflammatory demyelinating polyradiculoneuropathy(
CIDP) is a rare acquired
demyelinating disease of
peripheral nervous system(PNS), characterized by relapsing or progressive proximal and distal
muscle weakness with possible sensory loss. It is one of several chronic neuropathic
syndromes that are believed to have an autoimmune
etiology. We experienced a case of
CIDP in a 3-month-old boy associated with perianal
abscess by
Klebsiella pneumoniae who had a precipitous onset of symptoms after
anesthesia. He was treated with intravenous immunoglobuline with little improvement but showed a remarkable clinical and electrophysiologic improvement after
methylprednisolone pulse therapy. We
report this case with a brief
review of related
literature.