Umbilical vein varix has diverse clinical features and an unpredictable
course during the
pregnancy and/or perinatal period. We
report a rare case of isolated fetal
varix of the intra-abdominal
umbilical vein, which was associated with fetal
cardiomegaly. After
birth, the
umbilical vein varix remained with continuous
blood flow through the patent ductus venosus. In addition, persistent
cardiomegaly was complicated with an
atrial septal defect.