Rare case of idiopathic lymphocytic interstitial pneumonia exhibits good response to Mycophenolate Mofetil.

Lymphoid interstitial pneumonia (LIP) is a poorly understood lymphoproliferative disorder that can be idiopathic or associated with different conditions. LIP is considered to be steroid responsive. However, its response is mainly unpredictable with a high mortality rate. Here we describe a rare case of idiopathic LIP that shows clinical improvement to Mycophenolate Mofetil after intolerable side effects of high-dose steroids.