ABSTRACT
El liquen escleroso es un trastorno mucocutáneo que afecta típicamente a mujeres en la etapa posmenopáusica. Aunque es una entidad poco conocida por los pediatras, hasta un 7-15% de los casos se dan en niñas prepuberales. Presentamos 3 casos de niñas diagnosticadas de liquen escleroso. En todos los casos, el diagnóstico inicial fue erróneo; de ahí la importancia de conocer este cuadro (AU)
Lichen sclerosus is a chronic mucocutaneous disorder that affects typically post-menopausical women. Although it's not well known by pediatricians, up to 7-15% of all cases happen in pre-puberal girls. We reported three cases of lichen esclerosus. In all three cases, the initial diagnosis was wrong, so the importance of knowing this cutaneous disorder (AU)
Subject(s)
Humans , Female , Child, Preschool , Lichen Sclerosus et Atrophicus/diagnosis , Genital Diseases, Female/diagnosis , Diagnosis, Differential , Leukorrhea/diagnosisABSTRACT
Multicystic dysplasia is the most common type of renal cystic disease, and it is one of the most common causes of an abdominal mass in infants. The contralateral system is also frequently abnormal. The most commonly associated anomalies are contralateral ureteropelvic junction obstruction and contralateral vesicoureteral reflux. In a few cases, multicystic dysplasia involves a horseshoe kidney or one pole of a duplex kidney. We present a female patient diagnosed with this condition at 9 years old, when she was being studied due to recurrent abdominal pain. The renal function was normal.
Subject(s)
Kidney/abnormalities , Multicystic Dysplastic Kidney/complications , Child , Female , Humans , Multicystic Dysplastic Kidney/diagnosisABSTRACT
La displasia renal multiquística es la variedad más frecuente de enfermedad quística renal y una de las causas más comunes de masa abdominal en recién nacidos y lactantes. Las anomalías contralaterales que se asocian con más frecuencia son la estenosis de la unión pieloureteral y el reflujo vesicoureteral. En muy pocos casos, la displasia renal multiquística está presente en uno de los segmentos de un riñón "en herradura" o en uno de los polos, en el caso de un doble sistema. Presentamos el caso de una paciente portadora de esta asociación de malformaciones diagnosticada a los 9 años de edad al ser estudiada por tener dolor abdominal recurrente. La función renal fue normal (AU)
Multicystic dysplasia is the most common type of renal cystic disease, and it is one of the most common causes of an abdominal mass in infants. The contralateral system is also frequently abnormal. The most commonly associated anomalies are contralateral ureteropelvic junction obstruction and contralateral vesicoureteral reflux. In a few cases, multicystic dysplasia involves a horseshoe kidney or one pole of a duplex kidney. We present a female patient diagnosed with this condition at 9 years old, when she was being studied due to recurrent abdominal pain. The renal function was normal (AU)