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Cochlear implantation is relatively a safe procedure with a favorable outcome. Labyrinthine ossification is one of the rare complications that has been observed in some occasions post-cochlear implantation. This paper report two cases of Mondini inner ear malformation cochlear implant failure associated with labyrinthine ossification, mandating revision surgery, and a literature review focusing on the reported cases, risk factors, surgical and non-surgical measures to mitigate this complication and to improve overall cochlear implant outcomes.
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Objective To assess the quality of life (QoL) in Saudi children with cochlear implants (CI) and determine sociodemographic and clinical factors that have an impact on the perceived QoL. Methods A cross-sectional study is performed by comparing the QoL of Saudi toddlers and young CI recipients with normal children, using the Paediatric Quality of Life Inventory 4.0 - Generic core scale (PedsQLTM 4.0 - GCS). A self-administered questionnaire was sent to parents of paediatric patients, who had cochlear implantation at King Abdulaziz University Hospital (KAUH), from March 2016 to March 2018. Mothers of age-matched normal children who attended the obstetrics and gynaecology clinics at King Khalid University Hospital (KKUH), in November 2019 were considered as a control group. Results When children with CI and normal children PedsQLTM 4.0 - GCS subscales (physical, emotional, social, and school) and total functioning scores were compared, no single significant difference was noted between the groups. The sociodemographic and clinical factors that have an impact on the perceived QoL were: gender, birth order, and distance from the CI center. Emotional, social, psychosocial, and total functioning were the main dimensions affected. Conclusion The QoL of Saudi children with CI is comparable to those of normal children. However, among children with CI, gender, birth order, and distance from the CI center were found to have different effects on the QoL dimensions.
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INTRODUCTION: Odontomas are benign neoplasms originating from odontogenic tissues. Most of these masses are asymptomatic and can only be diagnosed correctly via radiological studies. Treatment of choice for management of odontoma involves surgical excision to prevent secondary complications and result in a favourable prognosis. CASE PRESENTATION: This paper presents a rare case of odontoma of the middle ear in a four-year-old girl. The mass caused unilateral conductive hearing loss and facial nerve entrapment. We shed light on the typically vague clinical presentations of odontomas, as well as the available options in terms of diagnostic imaging modalities and their outcomes. Standard management of odontoma was followed to improve prognosis and avoid relapse. The aim of highlighting this case is to report on unique clinical, radiographical, and histological findings. DISCUSSION: Retrotympanic odontomas are extremely rare. Only five cases in the English-language literature have investigated such an incident. All of the reviewed cases were asymptomatic and discovered only using radiological evidence. Two cases were managed surgically while the remainder were conservatively managed. CONCLUSION: In five of the six cases mentioned in the English-language literature (including this paper), odontomas occurred in the first decade of life, with an obvious female predilection. In one case, odontoma occurred in the third decade of life. Although odontoma is marked by its frequently benign origin, the absence of symptoms, and the necessity of surgical intervention, further studies are needed to analyse the different clinical pictures, and to allow these to add to what is currently known.
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Background Hearing impairment is found to be the most prevalent disabling condition worldwide. Early diagnosis is crucial to avoid speech and language delays and to ensure the best performance results after cochlear implant (CI) surgery. Universal newborn hearing screening is a way to recognize newborns with a hearing impairment with or without risk factors. In this article, we have studied the effect of the newborn hearing screening program on early presentation to a healthcare center and, hence, early intervention in patients with congenital hearing loss, and reviewed the international numbers. Objectives The objective of this study was to determine whether neonatal hearing screening in Saudi Arabia helped prelingually deaf children to present earlier or not. Design Retrospective cross-sectional review Setting King Abdullah Ear Specialist Center (KAESC), Riyadh, Saudi Arabia Subjects and methods We included all patients who presented to the CI committee for the first time at KAESC, between March 2016 and March 2018, and met the inclusion criteria. Data were retrieved through phone calls and patient files. The sample size was 242. Main outcomes The timing difference between those who were screened positive for hearing loss at birth versus patients who were screened negative or not screened at all. Results By far, patients who were screened positive for hearing loss presented earlier (p-value >0.001) to a healthcare center than those who were not screened at all or screened negative for hearing loss and they finished the journey to CI 17 months earlier than those who were not screened. On the other hand, those who were screened negative were not found to present later than those who were not screened. Conclusion Going with the international trend, screening was found to have a significant positive effect on age at presentation, diagnosis, hearing aid fitting, surgery, and, hence, performance after implantation. Testing false negative on screening did not show a significant further delay when compared to those who were not screened.
