Subject(s)
Cardiology/history , Hospitals, Pediatric , Child , Czechoslovakia , History, 20th Century , Hospitals, Pediatric/history , HumansABSTRACT
In a retrospective study the results of operations for hemodynamically severe ventricular septal defect were analyzed in 18 patients with a body weight below 10 kg who had been operated on over a period of two years at the Institute of Cardiovascular Diseases in Bratislava. The first group consisted of 12 children with the mean body weight of 6650 g in whom complete correction of the ventricular septal defect was carried out by means extracorporeal circulation. Ligation of the pulmonary artery was performed in 6 infants with the mean body weight of 3420 g (second group). Patients of both groups had a serious left-to-right shunt and marked pulmonary hypertension. An excellent operative result was obtained in 10 children after complete correction of the defect. Two patients of the first group and one patient of the second group died suffering from severe pulmonary hypertension. Surgical correction of the hemodynamically severe ventricular septal defect in early childhood is indicated when conservative treatment fails and should be carried out as an urgent procedure regardless the age and body weight of the patient.
Subject(s)
Heart Septal Defects, Ventricular , Cardiopulmonary Bypass , Child, Preschool , Heart Septal Defects, Ventricular/physiopathology , Heart Septal Defects, Ventricular/surgery , Humans , Infant , Ligation , Pulmonary Artery/surgery , Retrospective StudiesSubject(s)
Aortic Valve Stenosis/diagnosis , Cardiomyopathy, Hypertrophic/diagnosis , Echocardiography , Adolescent , Aortic Valve Stenosis/physiopathology , Cardiomyopathy, Hypertrophic/physiopathology , Child , Child, Preschool , Diagnosis, Differential , Heart Ventricles/physiopathology , Humans , InfantSubject(s)
Ebstein Anomaly/diagnosis , Adolescent , Child , Child, Preschool , Diagnosis, Differential , Female , Humans , Infant , MaleSubject(s)
Cardiomyopathy, Hypertrophic/diagnosis , Echocardiography , Adolescent , Child , Child, Preschool , Female , Humans , MaleSubject(s)
Aorta, Thoracic/abnormalities , Aortography , Esophagus/diagnostic imaging , Female , Humans , MaleABSTRACT
The authors describe 5 cases of an unusual variant of tetralogy of Fallot with a characteristic clinical course. Its most prominent clinical manifestations are recurrent and severe respiratory infections caused by compression of the inferior trachea and bronchi by a dilated pulmonary artery. Two of the patients died of irreversible respiratory insufficiency. Of the 3 surviving patients one is doing comparatively well.
Subject(s)
Heart Septal Defects, Ventricular/complications , Pulmonary Valve/abnormalities , Electrocardiography , Heart Septal Defects, Ventricular/diagnosis , Humans , Infant , Tetralogy of Fallot/diagnosisABSTRACT
In a group of 20 children with pulmonary arterial valvular stenosis the clinical and routine laboratory data were assessed before surgical correction and at intervals of 4-10 years afterwards. In all children successfully operated upon, the ECG signs of right ventricular hypertrophy disappeared. In 10 children of the group the haemodynamic indicators were determined in the postoperative period with the aid of right-heart microcatheterization at rest and during exercise. A success of the correction was manifested by a normalization of the pressure conditions in the right heart. Exercise did not raise them to pathological levels. A successful removal of the stenosis was also manifested by the actual values of the ejection volume and cardiac index, mainly in their increases during exercise. Heart microcatheterization proved to be an expedient method for determining the haemodynamic indicators at rest and during exercise in the long-term follow-up of patients after surgical correction of congenital pulmonary arterial stenosis as one of defects with a good postoperative outlook.
