ABSTRACT
OBJECTIVE: Moebiüs sequence is a pathology not very well understood regarding to the hearing status. The main goal of this study was to describe the audiologic findings in children and adolescent who carry Moebiüs sequence. METHOD: Participated in this study 17 children and adolescent, with age ranging from 3 to 13 years old. Prior to the testing, the family answered an interview. It was realized external auditory canal inspection, and the hearing testing (auditory instrumentation, pure tone audiometry, speech audiometry, immittanciometric measures, and otoacoustic emissions) on the participants. RESULTS: The auditory instrumentation evaluation (n=6) was present in all participants. The pure tone audiometry presented normal hearing levels in 75.0% of the tested ears, one ear with conductive hearing loss, two ears with sensory neural hearing loss, and one ear with mixed hearing loss. The tympanometric measures showed Type A tympanograms in 63.0% of the ears, Type B in 11.1%, Type C in 18.5%, and Type As in 7.4%. T the acoustic reflexes measure showed contralateral acoustic reflexes present in 50.0% of the ears, and ipsilateral acoustic reflexes present in 34.6% ears. The OAE results showed presence in 73.0%, for the TOAE, and 76.9% for the DPOAE. CONCLUSION: These results support the idea that there is no audiologic pattern for conductive hearing loss. The majority of the participants presented hearing in the normal range. Care should be taken in drawing conclusions regarding to auditory status of the individual with Moebiüs sequence, but what can be said is that not always those individuals present hearing loss.
Subject(s)
Hearing Loss, Conductive/diagnosis , Hearing Loss, Conductive/epidemiology , Hearing Loss, Sensorineural/diagnosis , Hearing Loss, Sensorineural/epidemiology , Mobius Syndrome/epidemiology , Acoustic Impedance Tests , Adolescent , Audiometry, Pure-Tone/instrumentation , Audiometry, Speech , Child , Child, Preschool , Female , Humans , Male , Otitis Media/diagnosis , Otitis Media/epidemiology , Otoacoustic Emissions, Spontaneous/physiology , Prevalence , Reflex, Acoustic/physiologyABSTRACT
A Seqüência de Moebiüs tem sido descrita como uma patologia envolvendo paralisia do VI e VII pares cranianos. O reflexo acústico é resposta à estimulação acústica de forte intensidade, através da contração dos músculos estapédio e tensor do tímpano. O VII par craniano é responsável pela inervação do músculo estapédio. Espera-se ausência de reflexos acústicos em alguns pacientes com a Seqüência. OBJETIVO: Descrever uma série de casos do resultado imitanciométrico dos portadores da Seqüência de Moebiüs. MATERIAL E MÉTODO: Participaram desta pesquisa 17 indivíduos identificados com Seqüência de Moebiüs, de ambos os sexos com idade variando entre 3 e 13 anos, todos submetidos à meatoscopia e imitanciometria. RESULTADOS: Os resultados indicaram timpanogramas do Tipo A na maioria das orelhas, demonstrando resultados compatíveis com funcionamento normal do músculo estapédio. Para o reflexo acústico contralateral, observou-se que metade das orelhas analisadas apresentou ausência de respostas. A outra metade apresentou reflexos acústicos contralaterais presentes. Os resultados do reflexo acústico ipsilateral se encontraram ausentes na maioria dos casos. CONCLUSÃO: Os resultados dos reflexos acústicos sugerem que esta medição pode demonstrar auxílio no prognóstico do comprometimento da lesão do VII par craniano, uma vez que metade dos participantes apresentou reflexos acústicos presentes.
Moebius Sequence has been described as a pathology which involves the VI and VII cranial nerves, causing facial palsy. Acoustic reflexes are elicited by a high intensity stimulation of the stapedius and the tensor tympani muscles. The VII cranial nerve is responsible for innervating the stapedius muscle. No acoustic reflexes are expected for individuals with this Sequence. AIM: To describe immittance findings in a series of individuals with Moebius Sequence. MATERIALS AND METHODS: We had 17 individuals with Moebius Sequence of both gender, with age raging from 3 to 13 years, who were submitted to otoscopy and immittance measures. RESULTS: The results of this study indicated a Type A tympanometry in the majority of the analyzed ears, demonstrating normal function of the stapedius muscle. For the contralateral acoustic reflexes we observed it present in 50 percent of the ears. The ipsilateral acoustic reflexes were absent in the majority of the ears. CONCLUSION: The results of the acoustic reflexes suggested that this measure could help in the prognosis of VII cranial nerve lesions, since half of the individual presented those reflexes.
Subject(s)
Adolescent , Child , Child, Preschool , Female , Humans , Male , Acoustic Impedance Tests , Mobius Syndrome/physiopathology , Reflex, Acoustic/physiology , Otoscopy , Reproducibility of ResultsABSTRACT
UNLABELLED: Moebius Sequence has been described as a pathology which involves the VI and VII cranial nerves, causing facial palsy. Acoustic reflexes are elicited by a high intensity stimulation of the stapedius and the tensor tympani muscles. The VII cranial nerve is responsible for innervating the stapedius muscle. No acoustic reflexes are expected for individuals with this Sequence. AIM: To describe immittance findings in a series of individuals with Moebius Sequence. MATERIALS AND METHODS: We had 17 individuals with Moebius Sequence of both gender, with age raging from 3 to 13 years, who were submitted to otoscopy and immittance measures. RESULTS: The results of this study indicated a Type A tympanometry in the majority of the analyzed ears, demonstrating normal function of the stapedius muscle. For the contralateral acoustic reflexes we observed it present in 50% of the ears. The ipsilateral acoustic reflexes were absent in the majority of the ears. CONCLUSION: The results of the acoustic reflexes suggested that this measure could help in the prognosis of VII cranial nerve lesions, since half of the individual presented those reflexes.
