ABSTRACT
El prurigo pigmentoso es una dermatosis inflamatoria infrecuente de etiología desconocida caracterizada por episodios recurrentes de pápulas eritematosas y pruriginosas que evolucionan hacia una intensa pigmentación reticulada. Se ha referido más frecuentemente en mujeres adultas jóvenes en Japón. Sólo se han descrito fuera de Japón unos 30 casos. Describimos una paciente española de 32 años que desarrolló una dermatosis pruriginosa con las características clínicas y hallazgos histopatológicos del prurigo pigmentoso. Se revisan las características epidemiológicas, clínicas e histopatológicas de esta peculiar enfermedad cutánea
Prurigo pigmentosa is an infrequent inflammatory dermatosis of unknown etiology, characterized by recurrent episodes of pruritic erythematous papules which develop into intense reticulated pigmentation. It has been referenced most frequently in young women in Japan. Only thirty cases have been described outside of Japan. We describe a 32-year-old Spanish female who developed a pruritic dermatosis with the clinical characteristics and histopathological findings of prurigo pigmentosa. We review the epidemiological, clinical and histopathological characteristics of this peculiar skin disease
Subject(s)
Female , Adult , Humans , Prurigo/physiopathology , Pigmentation Disorders/physiopathology , Hyperpigmentation/etiology , Biopsy , Sulfones/therapeutic use , Prurigo/drug therapyABSTRACT
Prurigo pigmentosa is an infrequent inflammatory dermatosis of unknown etiology, characterized by recurrent episodes of pruritic erythematous papules which develop into intense reticulated pigmentation. It has been referenced most frequently in young women in Japan. Only thirty cases have been described outside of Japan. We describe a 32-year-old Spanish female who developed a pruritic dermatosis with the clinical characteristics and histopathological findings of prurigo pigmentosa. We review the epidemiological, clinical and histopathological characteristics of this peculiar skin disease.