ABSTRACT
A 37-year-old lady presented with difficulty in breathing, which had progressively worsened in the last few months. Investigations revealed dextrocardia, congenitally corrected transposition of aorta, severe left atrioventricular valve stenosis with regurgitation, and right atrioventricular valve regurgitation. Left atrioventricular valve stenosis with thickening of leaflets and commissural fusion were suggestive of rheumatic valvular heart disease. She underwent left atrioventricular valve replacement and right atrioventricular valve repair with annuloplasty ring. This is a unique association of rheumatic valvular disease in corrected transposition of great arteries with dextrocardia. Morphology made surgical correction very challenging. Surgical correction of such case has not been reported in literature so far.
