1.
J Clin Neurosci
; 18(2): 171-80, 2011 Feb.
Article
in English
| MEDLINE
| ID: mdl-21215639
ABSTRACT
Von Hippel-Lindau disease is an inherited syndrome predisposing to a variety of benign and malignant neoplasms of the central nervous system and viscera that requires comprehensive screening and follow-up of individuals and their families. As such, it is important for the neurosurgeon to be aware of its clinical features and management issues. In this article we review the clinical aspects, management and surveillance of von Hippel-Lindau disease for neurosurgical practice.