ABSTRACT
Lipoblastoma and lipoblastomatosis are rare mesenchymal benign tumors of embryonal white fat. They are found primarily in children less than 5 years of age. This tumor presents in two forms: a localized well-circumscribed lesion (lipoblastoma), or a multicentric type (lipoblastomatosis). The authors presents three cases, two of them with a buttock lesion, the last with a paravertebral one. It is recommended a complete but conservative excision of the tumor because there is a natural tendency to involution, although in the first year of life a local reexcision for recurrence is sometimes described.
Subject(s)
Abdominal Neoplasms/surgery , Lipoma/surgery , Skin Neoplasms/surgery , Abdominal Neoplasms/diagnosis , Abdominal Neoplasms/pathology , Buttocks , Female , Humans , Infant , Infant, Newborn , Lipoma/diagnosis , Lipoma/pathology , Magnetic Resonance Imaging , Male , Skin/pathology , Skin Neoplasms/diagnosis , Skin Neoplasms/pathology , Tomography, X-Ray ComputedABSTRACT
The congenital cystic adenomatoid malformation (MACP), represents the congenital lung malformation most frequent in pediatric age. After examining the embryology, the treatment and the evolution of the malformation we wish to report our experience of four cases of MACP in patients 2 month, 1, 2 and 3 years of age. Lobectomy has cured all patients with the exception of one; this child had a MACP of the lung associated with Rhabdomyosarcoma and died after one and half year of chemotherapy.
