ABSTRACT
El carcinoma suprarrenal es una entidad poco frecuente y excepcional como productor de síndrome adrenogenital prepuberal. Sus criterios de malignidad, al igual que la eficacia de tratamiento adyuvante, son tema de discusión, lo que unido a su pronóstico sombrío mueve a la publicación de casos aislados de distintos grupos quirúrgicos en un intento de conocer esta patología. Presentamos un caso de carcinoma suprarrenal virilizante en paciente prepuberal tratado mediante suprarrenalectomía; la paciente se encuentra asintomática tras 5 años de la intervención (AU)
Subject(s)
Adolescent , Female , Humans , Hirsutism , Folliculitis , Hypertrophy , Clitoris/abnormalities , Adrenocortical Carcinoma/surgeryABSTRACT
We report a case of renal angiomyolipoma in a patient who, following normal delivery, presented with abdominal pain and acute abdomen with severe hemodynamic compromise that led to hypovolemic shock. Following diagnosis by emergency exploratory laparotomy, a left nephrectomy was performed. We underscore the difficulty involved in the diagnosis of acute abdomen from hemoperitoneum resulting from a ruptured angiomyolipoma, and highlight the rarity of this condition. Our patient was submitted to radical surgery because of vessel (hilum) invasion. The tumor was benign and no complications were observed. Patient work up eight years postoperatively revealed no local or systemic evidence of disease.
