ABSTRACT
Introducción: Se presenta un caso de tumor de partes blandas de patrón epitelioide, con rasgos clínicos, histológicos e inmunohistoquímicos acordes con la recientemente descrita "variante proximal" de sarcoma epitelioide. Material y métodos: Un varón de 28 años debuta con un tumor profundo localizado en la región perineal. Resultados: Microscópicamente, mostró hábito epitelioide, con marcada atipia citológica y frecuentes rasgos rabdoides, siendo el patrón de inmunoreactividad superponible al del sarcoma epitelioideclásico. Conclusiones: Ante un tumor con rasgos intermedios entre un sarcoma epitelioide clásico, un tumor rabdoide y un carcinoma indiferenciado, hay que pensar en la variante proximal del sarcoma epitelioide (AU)
Subject(s)
Adult , Male , Humans , Sarcoma/diagnosis , Sarcoma/pathology , Immunohistochemistry/methods , Perineum/pathology , Sarcoma, Clear Cell/diagnosis , Sarcoma, Clear Cell/pathology , Retroperitoneal Neoplasms/complications , Retroperitoneal Neoplasms/diagnosis , Retroperitoneal Neoplasms/epidemiology , Retroperitoneal Neoplasms/pathology , Sarcoma , Sarcoma/ultrastructureABSTRACT
OBJECTIVE: To report an additional case of retroperitoneal ganglioneuroma. METHODS/RESULTS: A case of retroperitoneal ganglioneuroma that had been incidentally discovered in a 27-year-old male during abdominal US evaluation is described. The diagnosis was based on the histopathological findings after US-guided biopsy. The clinical features and the findings of the complementary tests, which included radiological assessment, intravenous urography, CT and cavography are presented, as well as the pathology findings. Treatment was by complete surgical excision of the tumor. CONCLUSION: Treatment of ganglioneuroma is by surgery, since the diagnosis is generally based on the histopathological analysis of the surgical specimen. For those cases with a preoperative diagnosis, some authors advocate surgery for patients with clinical evidence of neuroblastoma or another pathology arising from this disease. Although infrequent, ganglioneuroma coexisting with neuroblastoma can occur. For this reason, complete excision of the tumor is preferred.
Subject(s)
Ganglioneuroma , Retroperitoneal Neoplasms , Adult , Ganglioneuroma/diagnosis , Humans , Male , Retroperitoneal Neoplasms/diagnosisABSTRACT
Granular cell tumor is an unusual growth of probably neuroectodermal histogenesis, first reported by Abrikossoff in 1926 with the name of myoblastoma. Of the about 1200 cases reported since, the 50 percent were found in the head and neck. Of second mentioned 10 percent had a laryngeal sitting. A case of glottic granular cell tumor surgically removed with free borders is presented. Bibliographical review.
