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Lupus ; 33(8): 886-891, 2024 Jul.
Article in English | MEDLINE | ID: mdl-38719778

ABSTRACT

In rare instances, patients with SLE may exhibit atypical clinical manifestations, such as Hypocomplementemic Urticarial Vasculitis, which can pose diagnostic challenges. Here, we present a case report of a 28-year-old female with a history of SLE with lupus nephritis clase IV who developed HUV-like symptoms, ultimately leading to a diagnosis of C1q Vasculitis. This case underscores the importance of considering C1q Vasculitis in SLE patients presenting with HUV-like features and highlights Rituximab as a promising therapeutic option for managing this rare condition.


Subject(s)
Complement C1q , Lupus Erythematosus, Systemic , Rituximab , Urticaria , Vasculitis , Humans , Female , Adult , Complement C1q/deficiency , Lupus Erythematosus, Systemic/complications , Lupus Erythematosus, Systemic/diagnosis , Vasculitis/diagnosis , Vasculitis/drug therapy , Urticaria/diagnosis , Rituximab/therapeutic use , Lupus Nephritis/diagnosis , Lupus Nephritis/complications , Lupus Nephritis/drug therapy , Diagnosis, Differential
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