ABSTRACT
The hip is considered to be one of the main load bearing joints of the body. In the haemophilic patient joint bleeds can be catastrophic, leading to long-term joint degeneration and accompanying arthritis. In this review we explore the mechanisms of joint destruction, with particular consideration of the anatomy of the hip and how it may influence disease progression. We also review current strategies for treatment including hip replacement in the haemophilic patient and describe our experiences as a unit. Finally we evaluate future prospects in the management of hip disease in haemophilia.
Subject(s)
Arthroplasty, Replacement, Hip/methods , Hemarthrosis/surgery , Hemophilia A/surgery , Hemostasis, Surgical/methods , Hip Joint/surgery , Osteoarthritis, Hip/surgery , Arthroplasty, Replacement, Hip/adverse effects , Hemarthrosis/complications , Hemophilia A/complications , Hemostasis, Surgical/adverse effects , Hip Joint/diagnostic imaging , Humans , Osteoarthritis, Hip/diagnostic imaging , Radiography , Secondary PreventionABSTRACT
The ankle joint is well known to show early involvement in severe haemophilia. We describe a novel operative technique developed by the senior author. This combines a medial approach to the ankle, medial malleolar osteotomy, bone graft and compression with staples. All patients had excellent pain relief and improvement in function with 100% achieving bony union. There was a significant improvement in Mazur ankle scores following ankle fusion (P < 0.01). This surgical technique gives good results which are reproducible in this patient population.
Subject(s)
Ankle Joint/surgery , Hemarthrosis/surgery , Hemophilia A/complications , Hemophilia B/complications , Adult , Ankle Joint/physiopathology , Arthrodesis/methods , Hemarthrosis/physiopathology , Humans , Male , Recovery of Function/physiology , Treatment OutcomeABSTRACT
There remains a relative paucity in the literature regarding upper limb manifestations of haemophilic arthropathy. Haemophilia has a wide range of clinical manifestations, often presenting with orthopaedic complications. These arise from multiple haemarthroses which exact a cumulative toll on the fabric of the joints. Although the lower limbs are predominantly affected due to their load-bearing nature, upper limb disease is common. This arises from the mechanical demands on the upper limb as the elbow and shoulder become partially weight bearing on use of walking aids such as elbow crutches.
Subject(s)
Biomechanical Phenomena/methods , Hemarthrosis/physiopathology , Hemophilia A/complications , Orthopedic Procedures/methods , Upper Extremity/physiopathology , Female , Hemarthrosis/surgery , Humans , Male , Upper Extremity/surgeryABSTRACT
We report two cases of this rare postoperative condition. Both patients having undergone extensive surgery to their hips, developed increased bone growth in the soft tissue of the hip, accounting for the reduced range of movement, pain and stiffness. Plain x-rays taken confirmed the presence of heterotopic ossification, also known as a variant of myositis ossificans. We review the literature and discuss treatment options of this rare condition in patients with end-stage haemophilic arthropathy.
