ABSTRACT
CASE REPORT: We describe the unusual diagnosis of a ciliary body medulloepithelioma by histopathology of a subretinal membrane obtained from vitreoretinal surgery of a 10-year-old boy. The patient had a history of perforating trauma OS 2 years earlier, and both fundus exam and B-scan ultrasound revealed only a retinal detachment with a subretinal membrane. No detectable mass was present. DISCUSSION: The membrane removed from underneath the peripheral retina revealed a blue cell tumor confirmed by histopathology and immunohistochemistry to be a primitive neuroectodermal tumor. Currently, the patient has been followed for 5 years with no signs of recurrence.
Subject(s)
Ciliary Body/pathology , Eye Injuries, Penetrating/complications , Neuroectodermal Tumors, Primitive/complications , Uveal Neoplasms/complications , Cataract/etiology , Child , Ciliary Body/surgery , Diagnosis, Differential , Eye Injuries, Penetrating/diagnostic imaging , False Negative Reactions , Follow-Up Studies , Humans , Light Coagulation , Male , Neuroectodermal Tumors, Primitive/diagnosis , Neuroectodermal Tumors, Primitive/pathology , Neuroectodermal Tumors, Primitive/surgery , Remission Induction , Retinal Detachment/diagnostic imaging , Retinal Detachment/etiology , Retinoblastoma/diagnosis , Time Factors , Tomography, X-Ray Computed , Ultrasonography , Uveal Neoplasms/diagnosis , Uveal Neoplasms/pathology , Uveal Neoplasms/surgery , VitrectomyABSTRACT
PURPOSE: The management of retinoblastoma has been shifting toward conservative treatment. Visual preservation has become a concern as tumor regression is achieved. To report the surgical approach and outcome of a radiation-induced cataract in an only eye with regressed retinoblastoma. METHODS: Single case report and review of literature. RESULTS: Small incision sutureless phacoemulsification and implant of an acrylic foldable intraocular lens was performed. Best-corrected visual acuity 1 year after surgery was 20/20. No tumor recurrence has been noted after 27 months of follow-up. CONCLUSIONS: Phacoemulsification and foldable intraocular lens implant seemed to be an appropriate therapeutic option for this case.
Subject(s)
Cataract/etiology , Lens Implantation, Intraocular/methods , Lens, Crystalline/radiation effects , Phacoemulsification/methods , Radiation Injuries/etiology , Retinal Neoplasms/radiotherapy , Retinoblastoma/radiotherapy , Child, Preschool , Humans , Lenses, Intraocular , Male , Radiotherapy/adverse effects , Remission Induction , Treatment OutcomeABSTRACT
OBJECTIVE: To compare standard color vision test results (Ishihara test) with a new test developed by the authors ("crayon" test) for the detection of congenital dyschromatopsia. METHODS: Cross-sectional study of 712 children from three public schools and one private school in the city of Porto Alegre, state of Rio Grande do Sul. Children with learning disabilities, or systemic and ocular diseases were excluded from this random sample. Two color vision tests, Ishihara test (short version with 14 plates) and crayon test (developed by the authors) were sequentially applied. Each test was applied by different evaluators and analyzed by a third evaluator. RESULTS: The crayon test showed a specificity of 100% (99.3-100%) and sensitivity of 38.5% (15.1-67.7%) when compared to Ishihara test. The prevalence of congenital dyschromatopsia in this population sample was 2.6% for male children, and 0.9% for female children. CONCLUSIONS: The crayon test results showed greater specificity than Ishihara test in the studied group; however, sensitivity was not adequate for a screening test. It is necessary to improve the sensitivity so that congenital dyschromatopsia can be detected by the crayon test.