ABSTRACT
Nutcracker syndrome is caused by compression of left renal vein between the aorta and the superior mesenteric artery. This phenomenon results in left renal venous hypertension, left gonadal vein varices and unilateral hematuria. We report a typical case of nutcracker syndrome and we review the literature in an effort to explain this pathology.
Subject(s)
Hematuria/etiology , Kidney Tubules, Collecting , Renal Artery , Adolescent , Humans , Kidney Diseases/diagnostic imaging , Kidney Diseases/etiology , Kidney Tubules, Collecting/diagnostic imaging , Male , Radiography , Renal Artery/diagnostic imaging , Syndrome , Vascular Diseases/complications , Vascular Diseases/diagnostic imagingABSTRACT
El síndrome del cascanueces está causado por una compresión de la vena renal entre la aorta y la arteria mesentérica superior. Este fenómeno resulta en una hipertensión de la vena renal izquierda, varices en la vena gonadal izquierda y hematuria unilateral. Comunicamos un caso típico de síndrome de cascanueces y se lleva a cabo una revisión de la literatura reciente para tratar de explicar esta patología (AU)
Nutcracker syndrome is caused by compression of left renal vein between the aorta and the superior mesenteric artery. This phenomenon results in left renal venous hypertension, left gonadal vein varices and unilateral hematuria. We report a typical case of nutcracker syndrome and we review the literature in an effort to explain this pathology (AU)
Subject(s)
Adolescent , Male , Humans , Renal Artery , Kidney Tubules, Collecting , Syndrome , Vascular Diseases , Kidney Diseases , HematuriaABSTRACT
Primary intimal angiosarcomas of the aorta (i.e. mostly intraluminal sarcomas with evidence of endothelial differentiation) are extraordinarily rare. We report a case in which the diagnosis was accurately made using immunohistochemistry in an intestinal resection specimen and confirmed during autopsy. The patient was a 64-year-old woman with mesenteric ischaemia and a "thrombus" in the abdominal aorta. Two segments of the ileum and the right colon were surgically removed. Histological examination showed multiple tumour emboli in small arteries of the submucosa, serosa and mesentery. The highly atypical cells comprising these emboli were positive immunohistochemically with antibodies to Ulex Europaeus, von Willebrand factor and CD31 and negative for CD34. During post-mortem examination, the intraaortic mass was located around the orifices of the coeliac and the superior mesenteric arteries, and gross tumour thrombi were found in the left renal and splenic arteries. This case emphasises the need for a wide panel of immunohistochemical antibodies when tumour emboli of unknown origin are under study.
